surgical experience with portal hypertension due to hepatoportal sclerosis (noncirrhotic portal fibrosis)

نویسندگان

sirus vakili from the department of surgery and medicine, tehran university of medical sciences, tehran, islamic republic of iran

mohammadjafar farahvash

چکیده

hepatoportal sclerosis or idiopathic portal hypertension has a worldwide distribution with prevalence in developing and temperate countries. of 64 patients with this disease seen during a twelve year period, 36 underwent splenectomy or a shunt procedure. the indications for surgical intervention were severe hypersplenism and persistent left upper abdominal pain andlorhistory of frequent episodes of esophageal bleeding. there were two operative deaths from uncontrollable bleeding. of 34 patients, none developed esophageal bleeding or encephalopathy on follow-ups ranging from one to 12 years. splenectomy in patients without bleeding was effective. proximal splenorenal shunt was also satisfactory in all cases. however, in the last few cases, warren's shunt has produced even more encouraging results. in addition to a general overview, features of this disease not previously discussed or emphasized in the literature, operative findings and surgical methods used, along with long-term results, are presented.

برای دانلود باید عضویت طلایی داشته باشید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

SURGICAL EXPERIENCE WITH PORTAL HYPERTENSION DUE TO HEPATOPORTAL SCLEROSIS (NONCIRRHOTIC PORTAL FIBROSIS)

Hepatoportal sclerosis or idiopathic portal hypertension has a worldwide distribution with prevalence in developing and temperate countries. Of 64 patients with this disease seen during a twelve year period, 36 underwent splenectomy or a shunt procedure. The indications for surgical intervention were severe hypersplenism and persistent left upper abdominal pain andlorhistory of frequent ep...

متن کامل

Noncirrhotic Portal Hypertension due to Nodular Regenerative Hyperplasia Treated with Surgical Portacaval Shunt

Nodular regenerative hyperplasia (NRH) is an uncommon condition, but an important cause of noncirrhotic intrahepatic portal hypertension (NCIPH), characterized by micronodules of regenerative hepatocytes throughout the liver without intervening fibrous septae. Herein, we present a case of a thirty-seven-year-old female with systemic lupus erythematosus (SLE) who was discovered to have significa...

متن کامل

Noncirrhotic portal fibrosis/idiopathic portal hypertension: APASL recommendations for diagnosis and treatment.

The Asian Pacific Association for the Study of the Liver (APASL) Working Party on Portal Hypertension has developed consensus guidelines on the disease profile, diagnosis, and management of noncirrhotic portal fibrosis and idiopathic portal hypertension. The consensus statements, prepared and deliberated at length by the experts in this field, were presented at the annual meeting of the APASL a...

متن کامل

Idiopathic noncirrhotic portal hypertension: current perspectives

The term idiopathic noncirrhotic portal hypertension (INCPH) has been recently proposed to replace terms, such as hepatoportal sclerosis, idiopathic portal hypertension, incomplete septal cirrhosis, and nodular regenerative hyperplasia, used to describe patients with a hepatic presinusoidal cause of portal hypertension of unknown etiology, characterized by features of portal hypertension (esoph...

متن کامل

Hepatoportal sclerosis: a cause of portal hypertension to bear in mind.

To the editor: Hepatoportal sclerosis (HS) is an idiopathic noncirrhotic intrahepatic portal hypertension characterized by splenomegaly, hypersplenism and portal hypertension. Although it is considered uncommon in developed countries there is an increasing number of cases reported which could traduce a better knowledge of this disease and a higher level of suspicion. Our objective is to report ...

متن کامل

Transjugular Intrahepatic Portosystemic Shunt for the Treatment of Portal Hypertension in Noncirrhotic Patients with Portal Cavernoma

Background. The purpose of this study was to evaluate the safety and efficacy of transjugular intrahepatic portosystemic shunt (TIPS) placement in the management of portal hypertension in noncirrhotic patients with portal cavernoma. Methods. We conducted a single institution retrospective analysis of 15 noncirrhotic patients with portal cavernoma treated with TIPS placement. 15 patients (4 wome...

متن کامل

منابع من

با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید


عنوان ژورنال:
medical journal of islamic republic of iran

جلد ۱، شماره ۱، صفحات ۵۰-۵۴

کلمات کلیدی

میزبانی شده توسط پلتفرم ابری doprax.com

copyright © 2015-2023